BLAAUW, BERT

BLAAUW, BERT  

Dipartimento di Scienze Biomediche - DSB  

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Risultati 1 - 20 di 103 (tempo di esecuzione: 0.05 secondi).
Titolo Data di pubblicazione Autori Rivista Serie Titolo libro
Reduced ATP turnover during hibernation in relaxed skeletal muscle 2025 De Napoli, CosimoMontesel, MauroCussonneau, LauraMarcucci, LorenzoGerminario, ElenaNarici, MarcoNogara, LeonardoBlaauw, Bert + NATURE COMMUNICATIONS - -
The novel use of the CFTR corrector C17 in muscular dystrophy: pharmacological profile and in vivo efficacy 2025 Benetollo, AlbertoParrasia, SofiaScano, MartinaBiasutto, LuciaRossa, AndreaNogara, LeonardoBlaauw, BertDalla Barba, FrancescoCaccin, PaolaCarotti, MarcelloAkyürek, Eylem EmekSacchetto, RobertaSandonà, Dorianna + BIOCHEMICAL PHARMACOLOGY - -
A Novel MAO-B/SSAO Inhibitor Improves Multiple Aspects of Dystrophic Phenotype in mdx Mice 2024 Gasparella FrancescaNogara LeonardoGerminario ElenaCiciliot StefanoVenegas Francisca CarolinaFontana FrancescaSales GabrieleSabbatini DanieleBlaauw BertCanton MarcellaVitiello Libero + ANTIOXIDANTS - -
Salbutamol repurposing ameliorates neuromuscular junction defects and muscle atrophy in Col6a1-/- mouse model of collagen VI-related myopathies 2024 Calabrò, SoniaNogara, LeonardoBizzotto, DarioBraghetta, PaolaRusso, LorisBlaauw, BertBonaldo, PaoloCescon, Matilde + CLINICAL AND TRANSLATIONAL MEDICINE - -
SEPN1-related myopathy depends on the oxidoreductase ERO1A and is druggable with the chemical chaperone TUDCA 2024 de Napoli, CosimoNogara, LeonardoPoggio, ElenaBrini, MarisaCALI, TITOBlaauw, Bert + CELL REPORTS MEDICINE - -
The mitochondrial ATP-dependent potassium channel (mitoKATP) controls skeletal muscle structure and function 2024 Di Marco, GiuliaGherardi, GaiaDe Mario, AgnesePiazza, IlariaBaraldo, MartinaMattarei, AndreaBlaauw, BertRizzuto, RosarioDe Stefani, DiegoMammucari, Cristina CELL DEATH & DISEASE - -
A combination of metformin and galantamine exhibits synergistic benefits in the treatment of sarcopenia 2023 Tezze, CaterinaAmendolagine, Francesco IvanNogara, LeonardoBaraldo, MartinaCiciliot, StefanoArcidiacono, DilettaZaramella, AliceMasiero, GiulioFerrarese, GiuliaBlaauw, BertSandri, Marco + JCI INSIGHT - -
Defective excitation-contraction coupling and mitochondrial respiration precede mitochondrial Ca2+ accumulation in spinobulbar muscular atrophy skeletal muscle 2023 Caterina MarchiorettiMarco PirazziniGaia GherardiLeonardo NogaraRoberta AndreottiPaolo MartiniLorenzo MarcucciMarta CanatoEmanuela ZuccaroCristina MammucariMarco PacificiAnna RaffaelloRosario RizzutoAndrea MattareiMarian A DesbatsLeonardo SalviatiAram MegighianGianni SorarùElena PegoraroElisa BelluzziAssunta PozzuoliCarlo BizPietro RuggieriChiara RomualdiMarco SandriBert BlaauwMaria Pennuto + NATURE COMMUNICATIONS - -
Sustained oral spermidine supplementation rescues functional and structural defects in COL6-deficient myopathic mice 2023 Metti S.Baraldo M.Castagnaro S.Cescon M.Blaauw B.Bonaldo P. + AUTOPHAGY - -
Activation of Akt-mTORC1 signalling reverts cancer-dependent muscle wasting 2022 Geremia, AlessiaSartori, RobertaBaraldo, MartinaNogara, LeonardoBalmaceda, ValeriaDumitras, Georgia AnaCiciliot, StefanoScalabrin, MarcoBlaauw, Bert + JOURNAL OF CACHEXIA, SARCOPENIA AND MUSCLE - -
CFTR corrector C17 is effective in muscular dystrophy, in vivo proof of concept in LGMDR3 2022 Martina ScanoAlberto BenetolloLeonardo NogaraMichela BondìFrancesco Dalla BarbaMichela SoardiAkyurek Eylem EmekPaola CaccinMarcello CarottiRoberta SacchettoBert BlaauwDorianna Sandonà + HUMAN MOLECULAR GENETICS - -
Inducible deletion of raptor and mTOR from adult skeletal muscle impairs muscle contractility and relaxation 2022 Baraldo, MartinaZorzato, SabrinaGeremia, AlessiaNogara, LeonardoDumitras, Ana GeorgiaCanato, MartaMarcucci, LorenzoBlaauw, Bert + THE JOURNAL OF PHYSIOLOGY - -
Signatures of muscle disuse in spaceflight and bed rest revealed by single muscle fiber proteomics 2022 Murgia, MartaCiciliot, StefanoReggiani, CarloSchiaffino, StefanoFranchi, Martino VToniolo, LuanaBlaauw, BertSandri, MarcoNarici, Marco V + PNAS NEXUS - -
Biofabricating murine and human myo-substitutes for rapid volumetric muscle loss restoration 2021 Vitiello, LiberoBlaauw, Bert + EMBO MOLECULAR MEDICINE - -
In vivo proof of concept of the efficacy of the CFTR corrector C17 in a sarcoglycanopathy mouse model 2021 Martina ScanoAlberto BenetolloLeonardo NogaraMichela BondìFrancesco Dalla BarbaPaola CaccinMarcello CarottiRoberta SacchettoBert BlaauwDorianna Sandonà - - Virtual meeting. Developmental Disorders: From Mechanism to Treatment
Molecular Mechanisms of Skeletal Muscle Hypertrophy 2021 Schiaffino S.Reggiani C.Blaauw B. + JOURNAL OF NEUROMUSCULAR DISEASES - -
Muscle functional recovery is driven by extracellular vesicles combined with muscle extracellular matrix in a volumetric muscle loss murine model 2021 Magarotto F.Andreetta M.Grassi M.Saggioro M.Nogara L.Tolomeo A. M.Francescato R.Collino F.Germano G.Caicci F.Maghin E.Piccoli M.Blaauw B.Gamba P.Muraca M.Pozzobon M. + BIOMATERIALS - -
PERM1 interacts with the MICOS-MIB complex to connect the mitochondria and sarcolemma via ankyrin B 2021 Romanello V.Nogara L.Blaauw B. + NATURE COMMUNICATIONS - -
Raptor is critical for increasing the mitochondrial proteome and skeletal muscle force during hypertrophy 2021 Nogara L.Tchampda Dondjang A. H.Geremia A.Blaauw B. + THE FASEB JOURNAL - -
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction (Frontiers in Cell and Developmental Biology, (2020), 8, (580933), 10.3389/fcell.2020.580933) 2021 Metti S.La Spina M.Braghetta P.Blaauw B. + FRONTIERS IN CELL AND DEVELOPMENTAL BIOLOGY - -