BRAGHETTA, PAOLA
BRAGHETTA, PAOLA
Dipartimento di Medicina Molecolare - DMM
Characterization of Proteome Changes in Aged and Collagen VI-Deficient Human Pericyte Cultures
2024 Moriggi, Manuela; Torretta, Enrica; Cescon, Matilde; Russo, Loris; Gregorio, Ilaria; Braghetta, Paola; Sabatelli, Patrizia; Faldini, Cesare; Merlini, Luciano; Gargioli, Cesare; Bonaldo, Paolo; Gelfi, Cecilia; Capitanio, Daniele
GBA1 inactivation in oligodendrocytes affects myelination and induces neurodegenerative hallmarks and lipid dyshomeostasis in mice
2024 Gregorio, Ilaria; Russo, Loris; Torretta, Enrica; Barbacini, Pietro; Contarini, Gabriella; Pacinelli, Giada; Bizzotto, Dario; Moriggi, Manuela; Braghetta, Paola; Papaleo, Francesco; Gelfi, Cecilia; Moro, Enrico; Cescon, Matilde
Salbutamol repurposing ameliorates neuromuscular junction defects and muscle atrophy in Col6a1-/- mouse model of collagen VI-related myopathies
2024 Calabrò, Sonia; Nogara, Leonardo; Jian, Yongzhi; Valentin, Manuel; Bizzotto, Dario; Braghetta, Paola; Russo, Loris; Gambarotto, Lisa; Blaauw, Bert; Hashemolhosseini, Said; Bonaldo, Paolo; Cescon, Matilde
Schwann Cell‐Specific Ablation of Beclin 1 Impairs Myelination and Leads to Motor and Sensory Neuropathy in Mice
2024 Gambarotto, Lisa; Russo, Loris; Bresolin, Silvia; Persano, Luca; D'Amore, Rachele; Ronchi, Giulia; Zen, Federica; Muratori, Luisa; Cani, Alice; Negro, Samuele; Megighian, Aram; Calabrò, Sonia; Braghetta, Paola; Bizzotto, Dario; Cescon, Matilde
Collagen VI promotes recovery from colitis by inducing lymphangiogenesis and drainage of inflammatory cells
2023 Molon, S.; Brun, P.; Scarpa, M.; Bizzotto, D.; Zuccolotto, G.; Scarpa, M.; Fassan, M.; Angriman, I.; Rosato, A.; Braghetta, P.; Castagliuolo, I.; Bonaldo, P.
Collagen VI sustains cell stemness and chemotherapy resistance in glioblastoma
2023 Cescon, M.; Rampazzo, E.; Bresolin, S.; Da Ros, F.; Manfreda, L.; Cani, A.; Della Puppa, A.; Braghetta, P.; Bonaldo, P.; Persano, L.
Emerging Perspectives on the Rare Tubulopathy Dent Disease: Is Glomerular Damage a Direct Consequence of ClC-5 Dysfunction?
2023 Priante, Giovanna; Ceol, Monica; Gianesello, Lisa; Bizzotto, Dario; Braghetta, Paola; Calò, Lorenzo; Del Prete, Dorella; Anglani, Franca
Ambra1 deficiency impairs mitophagy in skeletal muscle
2022 Gambarotto, Lisa; Metti, Samuele; Chrisam, Martina; Cerqua, Cristina; Sabatelli, Patrizia; Armani, Andrea; Zanon, Carlo; Spizzotin, Marianna; Castagnaro, Silvia; Strappazzon, Flavie; Grumati, Paolo; Cescon, Matilde; Braghetta, Paola; Trevisson, Eva; Cecconi, Francesco; Bonaldo, Paolo
Collagen VI deficiency causes behavioral abnormalities and cortical dopaminergic dysfunction
2022 Gregorio, Ilaria; Mereu, Maddalena; Contarini, Gabriella; Bello, Luca; Semplicini, Claudio; Burgio, Francesca; Russo, Loris; Sut, Stefania; Dall'Acqua, Stefano; Braghetta, Paola; Semenza, Carlo; Pegoraro, Elena; Papaleo, Francesco; Bonaldo, Paolo; Cescon, Matilde
Emilin-2 is a component of bone marrow extracellular matrix regulating mesenchymal stem cell differentiation and hematopoietic progenitors
2022 Da Ros, F.; Persano, L.; Bizzotto, D.; Michieli, M.; Braghetta, P.; Mazzucato, M.; Bonaldo, P.
EMILIN1 deficiency causes arterial tortuosity with osteopenia and connects impaired elastogenesis with defective collagen fibrillogenesis
2022 Adamo, Christin S; Beyens, Aude; Schiavinato, Alvise; Keene, Douglas R; Tufa, Sara F; Mörgelin, Matthias; Brinckmann, Jürgen; Sasaki, Takako; Niehoff, Anja; Dreiner, Maren; Pottie, Lore; Muiño-Mosquera, Laura; Gulec, Elif Yilmaz; Gezdirici, Alper; Braghetta, Paola; Bonaldo, Paolo; Wagener, Raimund; Paulsson, Mats; Bornaun, Helen; De Rycke, Riet; De Bruyne, Michiel; Baeke, Femke; Devine, Walter P; Gangaram, Balram; Tam, Allison; Balasubramanian, Meena; Ellard, Sian; Moore, Sandra; Symoens, Sofie; Shen, Joseph; Cole, Stacey; Schwarze, Ulrike; Holmes, Kathryn W; Hayflick, Susan J; Wiszniewski, Wojciech; Nampoothiri, Sheela; Davis, Elaine C; Sakai, Lynn Y; Sengle, Gerhard; Callewaert, Bert
Heart transcriptome profile of a novel transgenic mouse model for arrhythmogenic cardiomyopathy
2022 Calore, Martina; Compagno, Sofia; Vencato, Sara; Colpaert, Robin; Sacchetto, Claudia; Lorenzon, Alessandra; Becchi, Tommaso; Romualdi, Chiara; J de Windt, Leon; Braghetta, Paola; Vitiello, Libero; Rampazzo, Alessandra
Inactivation of Emilin-1 enhances cardiac fibrosis through TGF-beta and IL-1 beta pathways
2022 Braghetta, P; Facchinello, N; Pigato, G; Bizzotto, D; De Acutis, A; Cescon, M; Brun, P; Vozzi, G
Lack of COL6/collagen VI causes megakaryocyte dysfunction by impairing autophagy and inducing apoptosis
2022 Abbonante, Vittorio; Malara, Alessandro; Chrisam, Martina; Metti, Samuele; Soprano, Paolo; Semplicini, Claudio; Bello, Luca; Bozzi, Valeria; Battiston, Monica; Pecci, Alessandro; Pegoraro, Elena; De Marco, Luigi; Braghetta, Paola; Bonaldo, Paolo; Balduini, Alessandra
Ablation of collagen VI leads to the release of platelets with altered function
2021 Abbonante, V.; Gruppi, C.; Battiston, M.; Zulian, A.; Di Buduo, C. A.; Chrisam, M.; Sereni, L.; Laurent, P. -A.; Semplicini, C.; Lombardi, E.; Mazzucato, M.; Moccia, F.; Petronilli, V.; Villa, A.; Bello, L.; Pegoraro, E.; Bernardi, P.; Braghetta, P.; De Marco, L.; Bonaldo, P.; Balduini, A.
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction (Frontiers in Cell and Developmental Biology, (2020), 8, (580933), 10.3389/fcell.2020.580933)
2021 Metti, S.; Gambarotto, L.; Chrisam, M.; La Spina, M.; Baraldo, M.; Braghetta, P.; Blaauw, B.; Bonaldo, P.
Pathogenic Potential of Hic1-Expressing Cardiac Stromal Progenitors
2020 Soliman, H.; Paylor, B.; Scott, R. W.; Lemos, D. R.; Chang, C.; Arostegui, M.; Low, M.; Lee, C.; Fiore, D.; Braghetta, P.; Pospichalova, V.; Barkauskas, C. E.; Korinek, V.; Rampazzo, A.; Macleod, K.; Underhill, T. M.; Rossi, F. M. V.
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction
2020 Metti, S.; Gambarotto, L.; Chrisam, M.; Baraldo, M.; Braghetta, P.; Blaauw, B.; Bonaldo, P.
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signaling and miRNA dysregulation.
2019 Calore, Martina; Lorenzon, Alessandra; Vitiello, Libero; Poloni, Giulia; Khan Mohsin, Af; Beffagna, Giorgia; Dazzo, Emanuela; Sacchetto, Claudia; Polishchuk, Roman; Sabatelli, Patrizia; Doliana, Roberto; Carnevale, Daniela; Lembo, Giuseppe; Bonaldo, Paolo; De Windt, Leon; Braghetta, Paola; Rampazzo, Alessandra
Electrospun structures made of a hydrolyzed keratin-based biomaterial for development of in vitro tissue models
2019 Fortunato, G. M.; Da Ros, F.; Bisconti, S.; De Acutis, A.; Biagini, F.; Lapomarda, A.; Magliaro, C.; De Maria, C.; Montemurro, F.; Bizzotto, D.; Braghetta, P.; Vozzi, G.