BRAGHETTA, PAOLA
 Distribuzione geografica
Continente #
NA - Nord America 8.190
AS - Asia 3.420
EU - Europa 2.100
SA - Sud America 785
AF - Africa 738
OC - Oceania 84
Continente sconosciuto - Info sul continente non disponibili 31
Totale 15.348
Nazione #
US - Stati Uniti d'America 7.796
SG - Singapore 1.310
CN - Cina 676
BR - Brasile 509
IT - Italia 422
HK - Hong Kong 375
VN - Vietnam 266
DE - Germania 257
FI - Finlandia 197
SE - Svezia 118
PL - Polonia 116
GB - Regno Unito 93
FR - Francia 87
RU - Federazione Russa 83
NL - Olanda 78
IN - India 74
UA - Ucraina 69
AR - Argentina 67
BJ - Benin 50
MX - Messico 40
JP - Giappone 39
AT - Austria 38
ID - Indonesia 38
CA - Canada 36
ES - Italia 34
TR - Turchia 34
PE - Perù 31
EC - Ecuador 30
UZ - Uzbekistan 30
KZ - Kazakistan 28
RS - Serbia 28
ZA - Sudafrica 28
CR - Costa Rica 27
IE - Irlanda 27
SN - Senegal 27
GA - Gabon 26
CI - Costa d'Avorio 25
IQ - Iraq 25
MY - Malesia 25
NP - Nepal 25
TN - Tunisia 25
AL - Albania 24
CZ - Repubblica Ceca 24
IR - Iran 24
JM - Giamaica 24
KE - Kenya 24
MN - Mongolia 24
PH - Filippine 24
BO - Bolivia 23
CO - Colombia 23
DZ - Algeria 23
SA - Arabia Saudita 23
TW - Taiwan 23
BY - Bielorussia 22
CL - Cile 22
DK - Danimarca 22
GF - Guiana Francese 22
GP - Guadalupe 22
KR - Corea 22
PK - Pakistan 22
PS - Palestinian Territory 22
RO - Romania 22
TH - Thailandia 22
BF - Burkina Faso 21
GR - Grecia 21
HN - Honduras 21
HU - Ungheria 21
PY - Paraguay 21
SI - Slovenia 21
SO - Somalia 21
ZW - Zimbabwe 21
AU - Australia 20
AZ - Azerbaigian 20
BA - Bosnia-Erzegovina 20
IS - Islanda 20
LB - Libano 20
LY - Libia 20
NC - Nuova Caledonia 20
NZ - Nuova Zelanda 20
PT - Portogallo 20
SK - Slovacchia (Repubblica Slovacca) 20
VE - Venezuela 20
AO - Angola 19
BB - Barbados 19
BE - Belgio 19
BS - Bahamas 19
CM - Camerun 19
EG - Egitto 19
IL - Israele 19
KG - Kirghizistan 19
MK - Macedonia 19
NI - Nicaragua 19
RW - Ruanda 19
YT - Mayotte 19
BG - Bulgaria 18
CH - Svizzera 18
GE - Georgia 18
GM - Gambi 18
LC - Santa Lucia 18
MR - Mauritania 18
Totale 14.536
Città #
Fairfield 1.054
Ashburn 900
Woodbridge 836
Singapore 687
Houston 567
Chandler 544
Ann Arbor 466
Cambridge 405
Seattle 363
Hong Kong 355
Wilmington 345
Beijing 244
Jacksonville 225
Santa Clara 214
Boardman 136
Princeton 127
San Diego 107
Munich 102
Padova 101
Los Angeles 83
Des Moines 82
Ho Chi Minh City 76
Helsinki 74
Bytom 73
Hanoi 62
Nanjing 57
Roxbury 54
São Paulo 54
Medford 53
Cotonou 47
New York 40
Milan 38
Chicago 36
Turku 36
Buffalo 29
Dong Ket 28
Tashkent 28
Warsaw 28
Dakar 27
London 25
Tokyo 25
Libreville 24
Abidjan 23
Shenyang 23
Vienna 23
Stockholm 22
Nairobi 21
Ulan Bator 21
Jinan 20
San José 20
Bridgetown 19
Harare 19
Hefei 19
Kigali 19
Nanchang 19
Nassau 19
Noumea 19
Brooklyn 18
Lima 18
Managua 18
Nuremberg 18
Reykjavik 18
Baku 17
Castries 17
Kingston 17
Montreal 17
Rome 17
Amman 16
Belgrade 16
Bishkek 16
Luanda 16
Nouakchott 16
Dar es Salaam 15
Hebei 15
Johannesburg 15
Les Abymes 15
Minsk 15
Ouagadougou 15
Padua 15
Rio de Janeiro 15
Tripoli 15
Vientiane 15
Addis Ababa 14
Dublin 14
Dushanbe 14
Panama City 14
Phoenix 14
Pune 14
Riga 14
Shanghai 14
Tirana 14
Atlanta 13
Bamako 13
Conakry 13
Kuala Lumpur 13
Lusaka 13
Montevideo 13
Tbilisi 13
Tunis 13
Willemstad 13
Totale 9.811
Nome #
F-actin dynamics regulates mammalian organ growth and cell fate maintenance 335
Loss of mitochondrial calcium uniporter rewires skeletal muscle metabolism and substrate preference 253
PUBEX PUBSEX - A VERSATILE EXPRESSION VECTOR SYSTEM FOR PRODUCTION OF FUSION AND NONFUSION PROTEINS IN ESCHERICHIA-COLI 237
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 229
The ablation of the matricellular protein EMILIN2 causes defective vascularization due to impaired EGFR-dependent IL-8 production affecting tumor growth 226
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells. 221
NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models. 211
EMILIN3, an extracellular matrix molecule with restricted distribution in skin 207
First steps to define murine amniotic fluid stem cell microenvironment 205
Extracellular collagen VI has prosurvival and autophagy instructive properties in mouse fibroblasts 204
Cell type-specific transcription of the alpha 1(VI) collagen gene - Role of the AP1 binding site and of the core promoter 203
AMBRA1 Controls Regulatory T-Cell Differentiation and Homeostasis Upstream of the FOXO3-FOXP3 Axis 201
Distinct regions control transcriptional activation of the alpha1(VI) collagen promoter in different tissues of transgenic mice. 199
Ablation of collagen VI leads to the release of platelets with altered function 198
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy 197
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction 195
FGF signaling deregulation is associated with early developmental skeletal defects in animal models for mucopolysaccharidosis type II (MPSII). 192
Loss of EMILIN-1 Enhances Arteriolar Myogenic Tone Through TGF-β (Transforming Growth Factor-β)-Dependent Transactivation of EGFR (Epidermal Growth Factor Receptor) and Is Relevant for Hypertension in Mice and Humans 191
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signaling and miRNA dysregulation. 189
Overlapping, complementary and site-specific expression pattern of genes of the EMILIN/Multimerin family 187
A NEW RECOMBINANT DNA STRATEGY FOR THE MOLECULAR-CLONING OF RARE MEMBRANE-PROTEINS 186
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice 186
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy. 184
Wnt/b-catenin pathway in arrhythmogenic cardiomyopathy 184
Role of adiponectin in the metabolism of skeletal muscles in collagen VI–related myopathies 180
ISOLATION OF EMBRYONIC STEM (ES) CELLS IN MEDIA SUPPLEMENTED WITH RECOMBINANT LEUKEMIA INHIBITORY FACTOR (LIF) 180
Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies. 180
Emilin genes are duplicated and dynamically expressed during zebrafish embryonic development 179
EMILIN-3, a peculiar member of the EMILIN/Multimerin protein family, has a distinct expression pattern, forms oligomeric assemblies and serves as a pro TGF-β antagonist. 177
EMILIN-1 deficiency induces elastogenesis and vascular cell defects 176
An ultrastructural approach to the adaptive role of the cell wall in the intertidal algaFucus virsoides 176
Hmga2 promoter analysis in transgenic mice 174
Cationic PMMA nanoparticles bind and deliver antisense oligoribonucleotides allowing restoration of dystrophin expression in the mdx mouse. 172
Pathogenic Potential of Hic1-Expressing Cardiac Stromal Progenitors 171
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency 169
Multimerin-2 maintains vascular stability and permeability 169
Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency 166
Mechanisms of transcriptional activation of the Col6a1 gene during Schwann cell differentiation 165
Electrospun structures made of a hydrolyzed keratin-based biomaterial for development of in vitro tissue models 165
EXPRESSION CLONING OF PROTEINS ON MEMBRANE TRAFFIC PATHWAYS 163
Emilin1 links TGF-beta maturation to blood pressure homeostasis 163
Dystrophin restoration in skeletal, heart and skin arrector pili smooth muscle of mdx mice by ZM2 NP-AON complexes. 163
CELL-WALL ULTRASTRUCTURE AND CATION LOCALIZATION IN SOME BENTHIC MARINE-ALGAE 163
Vascular Smooth Muscle Emilin-1 Is a Regulator of Arteriolar Myogenic Response and Blood Pressure 161
NG2/CSPG4-collagen type VI interplays putatively involved in the microenvironmental control of tumour engraftment and local expansion. 158
Gelatin-genipin-based biomaterials for skeletal muscle tissue engineering 158
Mapping Wnt/beta-catenin signaling during mouse development and in colorectal tumors. 154
Expression of EMILIN-1 gene in mouse development 152
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′OMePS AON and ZM2 NP-AON Complexes in mdx Mice 150
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern 150
Collagen VI null mice as a model for early onset muscle decline in aging 148
O.14 Biocompatible nanoparticles as slow-release delivery system of 2′OMePS AON administered both intraperitoneally and orally in the mdx mice: dystrophin rescue and nanoparticles biodistribution 147
Analysis of beta cell proliferation dynamics in zebrafish 146
Biodistribution Studies of Polymeric Nanoparticles for Drug Delivery in Mice 146
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts 144
Ambra1 deficiency impairs mitophagy in skeletal muscle 143
Emerging Perspectives on the Rare Tubulopathy Dent Disease: Is Glomerular Damage a Direct Consequence of ClC-5 Dysfunction? 142
Preclinical PK and PD studies on 2'-O-methyl-phosphorothioate RNA antisense oligonucleotides in the mdx mouse model. 142
Lack of COL6/collagen VI causes megakaryocyte dysfunction by impairing autophagy and inducing apoptosis 138
Deep RNA profiling identified CLOCK and molecular clock genes as pathophysiological signatures in collagen VI myopathy 138
Collagen VI in healthy and diseased nervous system 138
Collagen VI sustains cell stemness and chemotherapy resistance in glioblastoma 137
Analysis of transcription of the Col6a1 gene in a specific set of tissues suggests a new variant of enhancer region 137
Muscle proteomics reveals novel insights into the pathophysiological mechanisms of collagen vi myopathies 137
Intracellular targetting signals of polymeric immunoglobulin receptors are highly conserved between species 136
Collagen VI deficiency causes behavioral abnormalities and cortical dopaminergic dysfunction 135
Emilin-2 is a component of bone marrow extracellular matrix regulating mesenchymal stem cell differentiation and hematopoietic progenitors 134
Analysis of regulatory regions of Emilin1 gene and their combinatorial contribution to tissue-specific transcription 131
Study of the molecular pathogenesis of arrhythmogenic cardiomyopathy due to Desmoglein-2 mutations: the zebrafish helps the mouse 128
S12.28 Rescue of myopathic collagen VI null mice by genetic inactivation of mitochondrial cyclophilin d 128
Targeting Interleukin-1β Protects from Aortic Aneurysms Induced by Disrupted Transforming Growth Factor β Signaling 127
Tissue-specific expression of promoter regions of the alpha1(VI) collagen gene in cell cultures and transgenic mice. 126
The expression of Emilin-1 in vascular smooth muscle cells regulates arteriolar myogenic response and blood pressure 126
Is beta-catenin signalling involved in the molecular pathogenesis of arrhythmogenic right ventricular cardiomyopathy? Study on DSG2 transgenic mice 126
The systemic administration of a low dose of 20MePS-AON combined with novel cationic polymethylmethacrylate nanoparticles induces the rescue of dystrophin expression in the mdx murine model 126
IDENTIFICATION, SEQUENCING AND EXPRESSION OF AN INTEGRAL MEMBRANE-PROTEIN OF THE TRANS-GOLGI NETWORK (TGN38) 124
M.P.1.01 Pilot trial with cyclosporin A in patients with collagen VI myopathies 124
T.P.22 Nanoparticles as delivery systems for antisense oligoribonucleotides: Biodistribution studies and definition of the release kinetic in treated mdx mice 124
Salbutamol repurposing ameliorates neuromuscular junction defects and muscle atrophy in Col6a1-/- mouse model of collagen VI-related myopathies 123
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction (Frontiers in Cell and Developmental Biology, (2020), 8, (580933), 10.3389/fcell.2020.580933) 120
P1.52 BIO-NMD: Discovery and validation of biomarkers for neuromuscular diseases (NMDs) – An EU funded FP7 project 117
Fra-2-expressing macrophages promote lung fibrosis in mice 115
GBA1 inactivation in oligodendrocytes affects myelination and induces neurodegenerative hallmarks and lipid dyshomeostasis in mice 111
Elastic fiber proteins in the glomerular mesangium in vivo and in culture 110
Biodistribution and molecular studies on orally administered nanoparticle-AON complexes encapsulated with alginate aiming at inducing dystrophin rescue in mdx mice. 110
COLLAGEN VI MYOPATHIES: FROM MOUSE THERAPY TO HUMAN TRIALS 108
Corrigendum: FGF signaling deregulation is associated with early developmental skeletal defects in animal models for mucopolysaccharidosis type II (MPSII) [Human Molecular Genetics, 27, 13, (2018) (2262-2275)] DOI: 10.1093/hmg/ddy131 107
Schwann Cell‐Specific Ablation of Beclin 1 Impairs Myelination and Leads to Motor and Sensory Neuropathy in Mice 107
Heart transcriptome profile of a novel transgenic mouse model for arrhythmogenic cardiomyopathy 106
EM.P.5.03 The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 99
Collagen VI promotes recovery from colitis by inducing lymphangiogenesis and drainage of inflammatory cells 96
EMILIN1 deficiency causes arterial tortuosity with osteopenia and connects impaired elastogenesis with defective collagen fibrillogenesis 94
EM.P.5.07 Abnormal elastin deposits and altered organization of elastic fibers in collagen VI- related disorders 94
Expression pattern and function analysis of Emilin genes in zebrafish 94
Inactivation of Emilin-1 enhances cardiac fibrosis through TGF-beta and IL-1 beta pathways 93
Characterization of Proteome Changes in Aged and Collagen VI-Deficient Human Pericyte Cultures 93
Mmrn2 null mice are hypertensive: dissecting the role of VSMCs and ECs 89
Tumor cell NG2 proteoglycan controls cancer progression through its interaction with host Collagen type VI 87
Ultrastructural and cytochemical study on pit connections of Pterocladia pinnata (Huds.) Papenf. (Gelidiales) 86
La questione animale: il caso della sperimentazione tra razionale scientifico e dibattito etico-pubblico 79
Totale 15.370
Categoria #
all - tutte 48.746
article - articoli 47.072
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 244
Totale 96.062


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021897 0 0 0 0 80 103 73 124 168 116 140 93
2021/20221.228 38 118 191 112 53 55 65 142 55 17 136 246
2022/20231.081 186 125 13 135 154 162 10 78 142 16 43 17
2023/2024678 44 81 84 51 67 98 43 45 23 29 50 63
2024/20252.643 12 175 117 95 374 86 151 269 222 111 429 602
2025/20265.176 565 822 1.237 1.627 925 0 0 0 0 0 0 0
Totale 15.433