FERNANDEZ-VIZARRA BAILEY, ERIKA MARIA
FERNANDEZ-VIZARRA BAILEY, ERIKA MARIA
Dipartimento di Scienze Biomediche - DSB
Mitochondrial translation is the primary determinant of secondary mitochondrial complex I deficiencies
2024 Čunátová, Kristýna; Vrbacký, Marek; Puertas-Frias, Guillermo; Alán, Lukáš; Vanišová, Marie; Saucedo-Rodríguez, María José; Houštěk, Josef; Fernández-Vizarra, Erika; Neužil, Jiří; Pecinová, Alena; Pecina, Petr; Mráček, Tomáš
Pathological variants in nuclear genes causing mitochondrial complex III deficiency: An update
2024 Čunátová, Kristýna; Fernández‐vizarra, Erika
Residual Complex I activity and amphidirectional Complex II operation support glutamate catabolism through mtSLP in anoxia
2024 Ravasz, Dora; Bui, David; Nazarian, Sara; Pallag, Gergely; Karnok, Noemi; Roberts, Jennie; Marzullo, Bryan P.; Tennant, Daniel A.; Greenwood, Bennett; Kitayev, Alex; Hill, Collin; Komlódi, Timea; Doerrier, Carolina; Cunatova, Kristyna; Fernandez-Vizarra, Erika; Gnaiger, Erich; Kiebish, Michael A.; Raska, Alexandra; Kolev, Krasimir; Czumbel, Bence; Narain, Niven R.; Seyfried, Thomas N.; Chinopoulos, Christos
CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B
2022 Brischigliaro, Michele; Cabrera-Orefice, Alfredo; Sturlese, Mattia; Elurbe, Dei M; Frigo, Elena; Fernandez-Vizarra, Erika; Moro, Stefano; Huynen, Martijn A; Arnold, Susanne; Viscomi, Carlo; Zeviani, Massimo
Cooperative assembly of the mitochondrial respiratory chain
2022 Fernández-Vizarra, Erika; Ugalde, Cristina
Editorial: Mitochondrial OXPHOS System: Emerging Concepts and Technologies and Role in Disease
2022 Fernández-Vizarra, Erika; Callegari, Sylvie; Garrabou, Glòria; Pacheu-Grau, David
Measurement of mitochondrial respiratory chain enzymatic activities in Drosophila melanogaster samples
2022 Brischigliaro, Michele; Frigo, Elena; Fernandez-Vizarra, Erika; Bernardi, Paolo; Viscomi, Carlo
Mitochondrial Cytochrome c Oxidase Defects Alter Cellular Homeostasis of Transition Metals
2022 Brischigliaro, Michele; Badocco, Denis; Costa, Rodolfo; Viscomi, Carlo; Zeviani, Massimo; Pastore, Paolo; Fernández-Vizarra, Erika
Two independent respiratory chains adapt OXPHOS performance to glycolytic switch
2022 Fernández-Vizarra, Erika; López-Calcerrada, Sandra; Sierra Magro, Ana; Pérez-Pérez, Rafael; Formosa Luke, E; Illescas, María; Peñas, Ana; Brischigliaro, Michele; Ding, Shujing; Fearnley Ian, M; Tzoulis, Charalampos; Pitceathly Robert, Ds; Martín Miguel, Angel; Stroud David, A; Zeviani, Massimo; Ryan Michael, T; Ugalde, Cristina
CEDAR, an online resource for the reporting and exploration of complexome profiling data
2021 van Strien, Joeri; Haupt, Alexander; Schulte, Uwe; Braun, Hans-Peter; Cabrera-Orefice, Alfredo; Choudhary, Jyoti S; Evers, Felix; Fernandez-Vizarra, Erika; Guerrero-Castillo, Sergio; Kooij, Taco W A; Páleníková, Petra; Pardo, Mercedes; Ugalde, Cristina; Wittig, Ilka; Wöhlbrand, Lars; Brandt, Ulrich; Arnold, Susanne; Huynen, Martijn A
Duplexing complexome profiling with SILAC to study human respiratory chain assembly defects
2021 Páleníková, Petra; Harbour, Michael E; Prodi, Federica; Minczuk, Michal; Zeviani, Massimo; Ghelli, Anna; Fernández-Vizarra, Erika
Inflammation causes remodeling of mitochondrial cytochrome c oxidase mediated by the bifunctional gene C15orf48
2021 Clayton, Sally A; Daley, Kalbinder K; Macdonald, Lucy; Fernandez-Vizarra, Erika; Bottegoni, Giovanni; O'Neil, John D; Major, Triin; Griffin, Daniel; Zhuang, Qinqin; Adewoye, Adeolu B; Woolcock, Kieran; Jones, Simon W; Goodyear, Carl; Elmesmari, Aziza; Filer, Andrew; Tennant, Daniel A; Alivernini, Stefano; Buckley, Christopher D; Pitceathly, Robert D S; Kurowska-Stolarska, Mariola; Clark, Andrew R
Loss of COX4I1 Leads to Combined Respiratory Chain Deficiency and Impaired Mitochondrial Protein Synthesis
2021 Čunátová, Kristýna; Reguera, David Pajuelo; Vrbacký, Marek; Fernández-Vizarra, Erika; Ding, Shujing; Fearnley, Ian M; Zeviani, Massimo; Houštěk, Josef; Mráček, Tomáš; Pecina, Petr
Mitochondrial disorders of the OXPHOS system
2021 Fernandez-Vizarra, Erika; Zeviani, Massimo
Mutation in the MICOS subunit gene APOO (MIC26) associated with an X-linked recessive mitochondrial myopathy, lactic acidosis, cognitive impairment and autistic features
2021 Benincá, Cristiane; Zanette, Vanessa; Brischigliaro, Michele; Johnson, Mark; Reyes, Aurelio; Valle, Daniel Almeida do; J Robinson, Alan; Degiorgi, Andrea; Yeates, Anna; Telles, Bruno Augusto; Prudent, Julien; Baruffini, Enrico; S F Santos, Mara Lucia; R de Souza, Ricardo Lehtonen; Fernandez-Vizarra, Erika; Whitworth, Alexander J; Zeviani, Massimo
NDUFS3 depletion permits complex I maturation and reveals TMEM126A/OPA7 as an assembly factor binding the ND4-module intermediate
2021 D'Angelo, Luigi; Astro, Elisa; De Luise, Monica; Kurelac, Ivana; Umesh-Ganesh, Nikkitha; Ding, Shujing; Fearnley, Ian M; Gasparre, Giuseppe; Zeviani, Massimo; Porcelli, Anna Maria; Fernandez-Vizarra, Erika; Iommarini, Luisa
Redox-Mediated Regulation of Mitochondrial Biogenesis, Dynamics, and Respiratory Chain Assembly in Yeast and Human Cells
2021 Geldon, Stefan; Fernández-Vizarra, Erika; Tokatlidis, Kostas
SILAC-based complexome profiling dissects the structural organization of the human respiratory supercomplexes in SCAFIKO cells
2021 Fernández-Vizarra, Erika; López-Calcerrada, Sandra; Formosa, Luke E; Pérez-Pérez, Rafael; Ding, Shujing; Fearnley, Ian M; Arenas, Joaquín; Martín, Miguel A; Zeviani, Massimo; Ryan, Michael T; Ugalde, Cristina
Biallelic mutations in NDUFA8 cause complex I deficiency in two siblings with favorable clinical evolution
2020 Tort, Frederic; Barredo, Estibaliz; Parthasarathy, Ranjani; Ugarteburu, Olatz; Ferrer-Cortès, Xenia; García-Villoria, Judit; Gort, Laura; González-Quintana, Adrián; Martín, Miguel A; Fernández-Vizarra, Erika; Zeviani, Massimo; Ribes, Antonia
Bioenergetic consequences from xenotopic expression of a tunicate AOX in mouse mitochondria: Switch from RET and ROS to FET
2020 Szibor, Marten; Gainutdinov, Timur; Fernandez-Vizarra, Erika; Dufour, Eric; Gizatullina, Zemfira; Debska-Vielhaber, Grazyna; Heidler, Juliana; Wittig, Ilka; Viscomi, Carlo; Gellerich, Frank; Moore, Anthony L