Fibrous dysplasia of the temporal bone

Fibrous dysplasia is a rare, benign disease even though the clinical picture may appear severe. It presents a progressive replacement of normal bone structures by fibrous tissue, can involve one or more bone segments and, in some cases, it could be associated with skin lesions and endocrinopathies (McCune-Albright syndrome). It manifests clinically with dysmorphic syndrome, ophthalmologic or otologic signs. We report three cases of temporal polyostotic fibrous dysplasia and we review the literature on this subject.