FERNANDEZ-VIZARRA BAILEY, ERIKA MARIA
 Distribuzione geografica
Continente #
NA - Nord America 566
AS - Asia 290
EU - Europa 143
SA - Sud America 6
AF - Africa 3
Totale 1.008
Nazione #
US - Stati Uniti d'America 562
SG - Singapore 202
CN - Cina 78
IT - Italia 34
GB - Regno Unito 33
DE - Germania 30
FR - Francia 10
NL - Olanda 10
ES - Italia 6
HK - Hong Kong 6
SI - Slovenia 6
FI - Finlandia 4
IE - Irlanda 4
AR - Argentina 3
IN - India 3
PT - Portogallo 3
BR - Brasile 2
CA - Canada 2
MX - Messico 2
SE - Svezia 2
AZ - Azerbaigian 1
DZ - Algeria 1
ML - Mali 1
PE - Perù 1
UA - Ucraina 1
ZA - Sudafrica 1
Totale 1.008
Città #
Singapore 147
Santa Clara 79
Boardman 64
Chandler 61
Ashburn 29
Beijing 28
Fairfield 25
London 16
Seattle 15
Houston 11
Woodbridge 11
Cambridge 10
Amsterdam 8
Padova 8
Wilmington 7
Hong Kong 6
Madrid 6
New York 6
Ann Arbor 4
Dublin 4
Helsinki 4
Ogden 4
Los Angeles 3
Luján 3
Porto 3
Arezzo 2
Bologna 2
Chiampo 2
Chiswick 2
Des Moines 2
Erlangen 2
Hackney 2
Hyderabad 2
Kilburn 2
Medford 2
Nanjing 2
Ottawa 2
Princeton 2
San Diego 2
Schio 2
Shenyang 2
Slough 2
Urbino 2
Acton 1
Arzignano 1
Baku 1
Berlin 1
Campinas 1
Cardiff 1
Dallas 1
Durban 1
Fontanelle 1
Kharkiv 1
Leeds 1
Lima 1
Milton Keynes 1
Mopti 1
Mérida 1
Nanchang 1
Orlando 1
Paese 1
Prescot 1
Pune 1
Ribeirão Preto 1
Roxbury 1
San Jose 1
Vicenza 1
Washington 1
Totale 623
Nome #
MPV17 encodes an inner mitochondrial membrane protein and is mutated in infantile hepatic mitochondrial DNA depletion 102
SURF1 knockout cloned pigs: Early onset of a severe lethal phenotype 66
CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B 30
Exome sequencing coupled with mRNA analysis identifies NDUFAF6 as a Leigh gene 29
Two independent respiratory chains adapt OXPHOS performance to glycolytic switch 29
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS 26
How do human cells react to the absence of mitochondrial DNA? 25
Knockdown of APOPT1/COA8 Causes Cytochrome c Oxidase Deficiency, Neuromuscular Impairment, and Reduced Resistance to Oxidative Stress in Drosophila melanogaster 25
Duplexing complexome profiling with SILAC to study human respiratory chain assembly defects 25
MPV17 encodes an inner mitochondrial membrane protein and is mutated in infantile hepatic mitochondrial DNA depletion 24
A homozygous MRPL24 mutation causes a complex movement disorder and affects the mitoribosome assembly 23
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III 22
Bioenergetic consequences from xenotopic expression of a tunicate AOX in mouse mitochondria: Switch from RET and ROS to FET 22
FASTKD2 nonsense mutation in an infantile mitochondrial encephalomyopathy associated with cytochrome c oxidase deficiency 22
Blue-Native Electrophoresis to Study the OXPHOS Complexes 22
Measurement of mitochondrial respiratory chain enzymatic activities in Drosophila melanogaster samples 22
Cooperative assembly of the mitochondrial respiratory chain 21
Two respiratory chain organizations with distinct bioenergetic properties coexist in human mitochondria 21
Assembly of the oxidative phosphorylation system in humans: what we have learned by studying its defects 21
In vitro transcription termination activity of the Drosophila mitochondrial DNA-binding protein DmTTF 19
Defective PITRM1 mitochondrial peptidase is associated with Aβ amyloidotic neurodegeneration 19
Infantile encephalopathy and defective mitochondrial DNA translation in patients with mutations of mitochondrial elongation factors EFG1 and EFTu 19
Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy 18
NDUFS3 depletion permits complex I maturation and reveals TMEM126A/OPA7 as an assembly factor binding the ND4-module intermediate 18
Mitochondrially-targeted APOBEC1 is a potent mtDNA mutator affecting mitochondrial function and organismal fitness in Drosophila 17
Loss of mitochondrial protease OMA1 alters processing of the GTPase OPA1 and causes obesity and defective thermogenesis in mice 17
Biallelic mutations in NDUFA8 cause complex I deficiency in two siblings with favorable clinical evolution 16
Mitochondrial Cytochrome c Oxidase Defects Alter Cellular Homeostasis of Transition Metals 16
Assembly of mammalian oxidative phosphorylation complexes I-V and supercomplexes 16
Mutations in APOPT1, encoding a mitochondrial protein, cause cavitating leukoencephalopathy with cytochrome c oxidase deficiency 15
Cavitating Leukoencephalopathy With Posterior Predominance Caused by a Deletion in the APOPT1 Gene in an Indian Boy 14
CEDAR, an online resource for the reporting and exploration of complexome profiling data 14
Five entry points of the mitochondrially encoded subunits in mammalian complex I assembly 13
Severe infantile encephalomyopathy caused by a mutation in COX6B1, a nucleus-encoded subunit of cytochrome c oxidase 12
COX7A2L Is a Mitochondrial Complex III Binding Protein that Stabilizes the III2+IV Supercomplex without Affecting Respirasome Formation 12
Mutation in the MICOS subunit gene APOO (MIC26) associated with an X-linked recessive mitochondrial myopathy, lactic acidosis, cognitive impairment and autistic features 12
COA7 (C1orf163/RESA1) mutations associated with mitochondrial leukoencephalopathy and cytochrome c oxidase deficiency 11
Mitochondrial gene expression is regulated at multiple levels and differentially in the heart and liver by thyroid hormones 10
Nonsense mutation in pseudouridylate synthase 1 (PUS1) in two brothers affected by myopathy, lactic acidosis and sideroblastic anaemia (MLASA) 10
Isolation of biogenetically competent mitochondria from mammalian tissues and cultured cells 10
Redox activation of mitochondrial intermembrane space Cu,Zn-superoxide dismutase 10
Editorial: Mitochondrial OXPHOS System: Emerging Concepts and Technologies and Role in Disease 10
MR-1S Interacts with PET100 and PET117 in Module-Based Assembly of Human Cytochrome c Oxidase 9
Inflammation causes remodeling of mitochondrial cytochrome c oxidase mediated by the bifunctional gene C15orf48 9
Tissue-specific differences in mitochondrial activity and biogenesis 9
Loss of COX4I1 Leads to Combined Respiratory Chain Deficiency and Impaired Mitochondrial Protein Synthesis 8
Inhibition of proteasome rescues a pathogenic variant of respiratory chain assembly factor COA7 8
In vivo and in organello analyses of mitochondrial translation 8
SURF1 knockout cloned pigs: Early onset of a severe lethal phenotype 8
Nuclear gene mutations as the cause of mitochondrial complex III deficiency 7
SILAC-based complexome profiling dissects the structural organization of the human respiratory supercomplexes in SCAFIKO cells 7
Redox-Mediated Regulation of Mitochondrial Biogenesis, Dynamics, and Respiratory Chain Assembly in Yeast and Human Cells 7
Mutations in NDUFB11, encoding a complex I component of the mitochondrial respiratory chain, cause microphthalmia with linear skin defects syndrome 7
LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells 6
Mitochondrial complex III Rieske Fe-S protein processing and assembly 6
Neuronal complex I deficiency occurs throughout the Parkinson's disease brain, but is not associated with neurodegeneration or mitochondrial DNA damage 6
Proteomics and gene expression analyses of mitochondria from squalene-treated apoE-deficient mice identify short-chain specific acyl-CoA dehydrogenase changes associated with fatty liver amelioration 6
Mitochondrial disorders of the OXPHOS system 6
Novel mutation in mitochondrial Elongation Factor EF-Tu associated to dysplastic leukoencephalopathy and defective mitochondrial DNA translation 6
Partial tandem duplication of mtDNA-tRNA(Phe) impairs mtDNA translation in late-onset mitochondrial myopathy 5
Isolation of mitochondria for biogenetical studies: An update 5
Supercomplex assembly determines electron flux in the mitochondrial electron transport chain 5
Totale 1.043
Categoria #
all - tutte 13.703
article - articoli 13.099
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 419
Totale 27.221


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2019/202048 0 0 0 0 0 0 8 8 9 13 8 2
2020/202145 6 2 6 2 0 5 1 7 7 3 2 4
2021/202227 0 0 8 1 0 3 0 4 0 2 4 5
2022/2023253 3 2 6 53 32 52 0 22 40 4 26 13
2023/2024283 12 28 24 31 30 21 37 7 15 5 43 30
2024/2025387 7 161 42 42 135 0 0 0 0 0 0 0
Totale 1.043