Enchondromas are frequent benign cartilaginous tumors that commonly arise in the hand. Ollier’s disease is defined by the presence of multiple enchondromas. Malignant transformation of an enchondroma is very rare in the hand. We present the case of a 19 years old girl affected by Ollier’s disease, with a rapidly growing enchondroma involving the middle finger with severe bone destruction and soft tissues infiltration. MRI of the hand demonstrated the presence of low signals in T1-weighted sequences and finely uneven medium-high intensity signal in T2-weighted sequences. Histology demonstrated a grade 1 chondrosarcoma, which was treated by a successful conservative surgical approach, with a strict follow-up due to the risk of possible recurrences.
Chondrosarcoma of the hand in olliers disease: case report and novel approach for surgical treatment
PIVATO, MATTIA;BERIZZI, ANTONIO;SIMONATO, FRANCESCA;CAPPELLESSO, ROCCO;SALVIATI, LEONARDO;FASSINA, AMBROGIO
2014
Abstract
Enchondromas are frequent benign cartilaginous tumors that commonly arise in the hand. Ollier’s disease is defined by the presence of multiple enchondromas. Malignant transformation of an enchondroma is very rare in the hand. We present the case of a 19 years old girl affected by Ollier’s disease, with a rapidly growing enchondroma involving the middle finger with severe bone destruction and soft tissues infiltration. MRI of the hand demonstrated the presence of low signals in T1-weighted sequences and finely uneven medium-high intensity signal in T2-weighted sequences. Histology demonstrated a grade 1 chondrosarcoma, which was treated by a successful conservative surgical approach, with a strict follow-up due to the risk of possible recurrences.
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