BONALDO, PAOLO
 Distribuzione geografica
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Continente #
NA - Nord America 14.160
EU - Europa 1.547
AS - Asia 1.504
OC - Oceania 8
SA - Sud America 8
AF - Africa 4
Continente sconosciuto - Info sul continente non disponibili 2
Totale 17.233
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Nazione #
US - Stati Uniti d'America 14.141
CN - Cina 838
SG - Singapore 516
IT - Italia 470
FI - Finlandia 307
DE - Germania 164
SE - Svezia 145
GB - Regno Unito 131
UA - Ucraina 121
FR - Francia 111
IN - India 63
VN - Vietnam 53
NL - Olanda 24
IE - Irlanda 22
HK - Hong Kong 19
CA - Canada 17
ES - Italia 10
RU - Federazione Russa 10
GR - Grecia 8
AU - Australia 7
BR - Brasile 7
BE - Belgio 4
NO - Norvegia 4
AT - Austria 3
HR - Croazia 3
IL - Israele 3
TR - Turchia 3
CH - Svizzera 2
EU - Europa 2
IR - Iran 2
MA - Marocco 2
MX - Messico 2
AR - Argentina 1
BD - Bangladesh 1
BG - Bulgaria 1
BY - Bielorussia 1
CZ - Repubblica Ceca 1
HU - Ungheria 1
JP - Giappone 1
KH - Cambogia 1
KR - Corea 1
KZ - Kazakistan 1
LU - Lussemburgo 1
MM - Myanmar 1
NG - Nigeria 1
NZ - Nuova Zelanda 1
PK - Pakistan 1
PL - Polonia 1
RO - Romania 1
SC - Seychelles 1
SI - Slovenia 1
Totale 17.233
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Città #
Fairfield 2.231
Woodbridge 1.894
Houston 1.301
Ann Arbor 1.108
Chandler 1.025
Ashburn 937
Seattle 758
Cambridge 742
Wilmington 703
Jacksonville 548
Singapore 410
Boardman 298
Santa Clara 293
Princeton 291
San Diego 233
Beijing 205
Des Moines 150
Helsinki 140
Padova 138
Nanjing 115
Medford 112
Roxbury 106
Guangzhou 57
Dong Ket 53
New York 51
Hebei 39
Shenyang 34
Nanchang 32
Jinan 28
London 26
Milan 24
Norwalk 24
Pune 21
Changsha 20
Jiaxing 20
Shanghai 20
Redwood City 19
Dublin 18
Ogden 18
Rome 16
Tianjin 15
Falls Church 14
Los Angeles 12
Zhengzhou 12
Paris 11
Dallas 10
Munich 10
Ningbo 10
Detroit 9
Hong Kong 9
Kilburn 9
Tappahannock 9
Haikou 8
Indiana 8
Aprilia 7
Hounslow 7
Lappeenranta 7
Selvazzano Dentro 7
Hefei 6
Kharkiv 6
Phoenix 6
Washington 6
Arlington 5
Barcelona 5
Borås 5
Camparada 5
Chengdu 5
Ottawa 5
Vicenza 5
Cadillac 4
Chiampo 4
Fuzhou 4
Groningen 4
Hangzhou 4
Kunming 4
Lanzhou 4
Lipomo 4
Taizhou 4
Wuhan 4
Brussels 3
Catania 3
Chiswick 3
Ferrara 3
Florence 3
Hanover 3
Magenta 3
Miami 3
Montreal 3
Montréal 3
Orange 3
Portland 3
Prescot 3
Rockville 3
Southwark 3
Stockholm 3
Taiyuan 3
Treviso 3
Turin 3
Yellow Springs 3
Abano Terme 2
Totale 14.593
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Nome #
Zebrafish ambra1a and ambra1b knockdown impairs skeletal muscle development 191
Perturbations in cell signaling elicit early cardiac defects in mucopolysaccharidosis type II 188
The epg5 knockout zebrafish line: a model to study Vici syndrome 188
Glycolytic-to-oxidative fiber-type switch and mTOR signaling activation are early-onset features of SBMA muscle modified by high-fat diet 170
The ablation of the matricellular protein EMILIN2 causes defective vascularization due to impaired EGFR-dependent IL-8 production affecting tumor growth 166
Loss of mitochondrial calcium uniporter rewires skeletal muscle metabolism and substrate preference 164
The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice 151
Physical exercise stimulates autophagy in normal skeletal muscles but is detrimental for collagen VI deficient muscles. 151
Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1 148
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration. 147
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies. 146
Lack of Collagen VI Promotes Wound-Induced Hair Growth 141
Transcription Factor EB Controls Metabolic Flexibility during Exercise 137
Collagen VI Ablation Retards Brain Tumor Progression Due to Deficits in Assembly of the Vascular Basal Lamina 137
Distinct regions control transcriptional activation of the alpha1(VI) collagen promoter in different tissues of transgenic mice. 136
Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition) 136
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells. 135
Autosomal recessive myosclerosis myopathy is a collagen VI disorder 131
Collagen VI regulates peripheral nerve regeneration by modulating macrophage recruitment and polarization 127
AMBRA1 Controls Regulatory T-Cell Differentiation and Homeostasis Upstream of the FOXO3-FOXP3 Axis 127
Multiple forms of chicken alpha3(VI) collagen chain generated by alternative splicing in type A repeated domains. 122
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy 121
Isolation of cDNA clones corresponding to the Mr=150,000 subunit of chick type VI collagen. 120
EMILIN3, an extracellular matrix molecule with restricted distribution in skin 120
Altered Threshold of the Mitochondrial Permeability Transition Pore in Ullrich Congenital Muscular Dystrophy 119
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial 119
Genetic ablation of cyclophilin D rescues mitochondrial defects and prevents muscle apoptosis in collagen VI myopathic mice. 118
First steps to define murine amniotic fluid stem cell microenvironment 118
Identification and characterization of novel collagen VI non-canonical splicing mutations causing ullrich congenital muscular dystrophy. 116
Emilin genes are duplicated and dynamically expressed during zebrafish embryonic development 116
Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies 116
Overlapping, complementary and site-specific expression pattern of genes of the EMILIN/Multimerin family 116
Collagen VI is required for the structural and functional integrity of the neuromuscular junction 115
Emilin3 is required for notochord sheath integrity and interacts with Scube2 to regulate notochord-derived Hedgehog signals. 114
Loss of EMILIN-1 Enhances Arteriolar Myogenic Tone Through TGF-β (Transforming Growth Factor-β)-Dependent Transactivation of EGFR (Epidermal Growth Factor Receptor) and Is Relevant for Hypertension in Mice and Humans 114
Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency 114
Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins 113
Fine-tuning of ULK1 mRNA and protein levels is required for autophagy oscillation 113
Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies. 113
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy. 112
Collagen VI regulates satellite cell self-renewal and muscle regeneration 112
O.14 Biocompatible nanoparticles as slow-release delivery system of 2′OMePS AON administered both intraperitoneally and orally in the mdx mice: dystrophin rescue and nanoparticles biodistribution 111
NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models. 111
Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial 111
Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies 110
EMILIN-1 deficiency induces elastogenesis and vascular cell defects 109
Cyclosporin A promotes in vivo myogenic response in collagen VI-deficient myopathic mice 109
Cationic PMMA nanoparticles bind and deliver antisense oligoribonucleotides allowing restoration of dystrophin expression in the mdx mouse. 108
Multiple binding reactivities of an IgG1 mouse monoclonal antibody raised against the extracellular matrix glycoprotein gp 115. 108
Dystrophin restoration in skeletal, heart and skin arrector pili smooth muscle of mdx mice by ZM2 NP-AON complexes. 106
Autophagy-mediated regulation of macrophages and its applications for cancer. 106
Aggresome-autophagy involvement in a sarcopenic patient with rigid spine syndrome and a p.C150R mutation in FHL1 gene 106
Mechanisms of transcriptional activation of the Col6a1 gene during Schwann cell differentiation 105
Altered Trabecular Bone Structure and Delayed Cartilage Degeneration in the Knees of Collagen VI Null Mice 105
Collagen VI-NG2 axis in human tendon fibroblasts under conditions mimicking injury response 104
A novel murine model for arrhythmogenic cardiomyopathy points to a pathogenic role of Wnt signaling and miRNA dysregulation. 104
Three novel collagen VI chains with high homology to the α3 chain 104
Collagen VI in cancer and its biological mechanisms. 103
Altered expression of the MCSP/NG2 chondroitin sulfate proteoglycan in collagen VI deficiency 101
Autosomal recessive Bethlem myopathy 101
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern 101
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts 100
Collagen VI regulates peripheral nerve myelination and function. 100
Gelatin-genipin-based biomaterials for skeletal muscle tissue engineering 100
Persistent Dystrophin Protein Restoration 90 Days after a Course of Intraperitoneally Administered Naked 2′OMePS AON and ZM2 NP-AON Complexes in mdx Mice 99
Evidence for the stochastic integration of gene trap vectors into the mouse germline. 99
Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency 99
Lack of collagen VI promotes neurodegeneration by impairing autophagy and inducing apoptosis during aging 98
The human type VI collagen gene: mRNA and protein variants of the alpha3 chain generated by alternative splicing of an additional 5'-end exon. 97
Muscle proteomics reveals novel insights into the pathophysiological mechanisms of collagen vi myopathies 97
Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies 97
The Polyphenol Pterostilbene Ameliorates the Myopathic Phenotype of Collagen VI Deficient Mice via Autophagy Induction 97
Biosynthesis of chick type VI collagen. I: Intracellular assembly and molecular structure. 96
Gene trap expression and mutational analysis for genes involved in the development of the mammalian nervous system. 96
Absence of Type VI Collagen Paradoxically Improves Cardiac Function, Structure, and Remodeling After Myocardial Infarction 96
Characterization of a rare case of Ullrich congenital muscular dystrophy due to truncating mutations within the COL6A1 gene C-terminal domain: a case report. 96
Structural and Functional Features of the α3 Chain Indicate a Bridging Role for Chicken Collagen VI in Connective Tissues 96
Dysfunctional tendon collagen fibrillogenesis in collagen VI null mice. 95
The Role of Collagens in Peripheral Nerve Myelination and Function 95
Differential and restricted expression of novel collagen VI chains in mouse. 94
Autophagy in Skeletal Muscle Homeostasis and in Muscular Dystrophies 94
Stable expression of chicken type VI collagen alpha1, alpha2, and alpha3 cDNAs in murine NIH/3T3 cells. 93
Adipocyte-derived collagen VI affects early mammary tumor progression in vivo, demonstrating a critical interaction in the tumor/stroma microenvironment. 93
Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies. 93
Structure, chromosomal localization, and promoter analysis of the human Elastin Microfibril Interfase Located proteIN (EMILIN) gene 92
Expression of EMILIN-1 gene in mouse development 91
Collagen VI at a glance 91
EMILIN-3, a peculiar member of the EMILIN/Multimerin protein family, has a distinct expression pattern, forms oligomeric assemblies and serves as a pro TGF-β antagonist. 91
Targeting of EMILIN-1 and EMILIN-2 to Fibrillin Microfibrils Facilitates their Incorporation into the Extracellular Matrix 90
Antisense-Induced Messenger Depletion Corrects a COL6A2 Dominant Mutation in Ullrich Myopathy. 90
Monoclonal antibodies for the different chains of chick type VI collagen. 88
Extracellular matrix: A dynamic microenvironment for stem cell niche. 88
Cyclosporine A in Ullrich congenital muscular dystrophy: long-term results. 87
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis 87
Cardiac glycoside ouabain induces autophagic cell death in non-small cell lung cancer cells via a JNK-dependent decrease of Bcl-2 87
Autophagy is Impaired in the Tibialis Anterior of Dystrophin Null Mice. 87
Deep RNA profiling identified CLOCK and molecular clock genes as pathophysiological signatures in collagen VI myopathy 87
Role of macrophages in Wallerian degeneration and axonal regeneration after peripheral nerve injury. 86
Extracellular collagen VI has prosurvival and autophagy instructive properties in mouse fibroblasts 86
Multimerin-2 maintains vascular stability and permeability 86
Totale 11.215
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Categoria #
all - tutte 65.088
article - articoli 62.777
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 557
selected - selezionate 0
volume - volumi 1.260
Totale 129.682
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Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2019/20202.164 0 0 0 0 0 275 326 429 384 378 252 120
2020/20212.306 105 155 118 228 139 157 142 240 331 219 287 185
2021/20222.668 95 304 397 209 106 107 141 333 92 44 312 528
2022/20232.047 402 233 47 242 350 263 4 127 224 22 100 33
2023/20241.168 75 163 149 92 92 138 86 54 43 49 111 116
2024/20251.473 32 317 191 173 669 91 0 0 0 0 0 0
Totale 17.395